TABLE 1

Clinical characteristics of patients with hyperinsulinism

Patient 1Patient 2Patient 3
Birth weight (g)5,9004,2004,055
Gestational age (weeks)39/4037/4036/40
Age of presentation (days)121
Maximum glucose infusion rate (mg · kg−1 · min−1)2512.511
Glucagon infusion requiredYesYesYes
Diazoxide responsive dose (mg · kg−1 · day−1)10106
Family history of diabetesYesYesYes
Attempted withdrawal of diazoxideNot successful at 7 monthsNot successful at 18 monthsSuccessful at 32 months